From: Use of rituximab in idiopathic retroperitoneal fibrosis
Characteristic | No. (%) |
---|---|
No. of patients | 10 |
Age of onset, yearsa | 58.5 ± 11.6 |
Gender | |
Male | 8 (80) |
Female | 2 (20) |
Presenting Symptoms | |
Flank Pain | 4 (40) |
Abdominal Pain | 2 (20) |
Nausea | 2 (20) |
Incidental Finding | 2 (20) |
Back Pain | 1 (10) |
Constipation | 1 (10) |
Weight Loss | 1 (10) |
Polyuria | 1 (10) |
Baseline Lab Parameters | |
IgG4 (g/L) | 0.1–4.6 |
CRP (mg/L) | 1.7–44.1 |
WBC (109/L) | 8.9 ± 2.5 |
Hematocrit (L/L) | 0.42 ± 0.36 |
Albumin (g/L) | 40.0 ± 2.7 |
Creatinine (umol/L) | 105.3 ± 19.7 |
Biopsy Proven Disease | |
Idiopathic RPF | 9 (90) |
Biopsy Declined | 1 (10) |
Past Treatment History | |
Prednisone | 4 (40) |
Azathioprine | 3 (30) |
Disease Duration Pre-Rituximab, monthsa | 17 ± 13 |
Concurrent Treatment with Rituximab | |
Prednisone | 3 (30) |
None | 7 (70) |