A. Common symptoms | |
1. Raynaud’s phenomenon | |
2. “Swollen”/“puffy” fingers or hands | |
B. Anti-U1snRNP antibodies | |
C. Miscellaneous | |
1. Lupus Manifestations | |
a. Polyarthritis | |
b. Adenopathies | |
c. Malar erythema | |
d. Serositis (pleuritis or pericarditis) | |
e. Cytopenia (leukopenia or thrombocytopenia) | |
2. Sclerodermiform manifestations | |
a. Sclerodactyly | |
b. Pulmonary fibrosis, restriction or decrease of diffusion < 70% c. Hypomotility or oesophageal dilation | |
3. Myositis | |
a. Muscular weakness | |
b. Muscle enzymes (CK) increase | |
c. Myopathic pattern on EMG |